Clinico-pathological Spectrum of Congenital Constriction Ring Syndrome and It’s Management

Abstract

Objective: To describe in detail, the spectrum of congenital Constriction Ring Syndrome (CRS), or amniotic band syndrome and its unique presentations. Since it is a relatively rare condition, and we have compared with existing literature, the knowledge of such a vast spectrum will help the clinicians in diagnosis and treatment.
Method: The study was done over a period of 3-years. Data regarding patient’s demographic profile, surgical procedure and outcomes were collected from previous records from January 2020 to April 2023. Demographic characters, limb involvement, distal deformities, surgical procedure etc were evaluated.
Result: Total of 48 rings in 33 patients were analysed. minimum and maximum reported age range was newborn to 16-years, mostly within 1-year, with female preponderance. Lower limb was affected more than upper limb, with a right sided predominance. Lymphoedema was most common complications, and all patients were managed surgically.
Conclusion: CRS is a rare entity. Timely and adequate management must prevent lifelong deformity. Detailed knowledge of spectrum and treatment protocol will help the clinician in satisfactory management of such patients.